OHVIRA Syndrome
نویسندگان
چکیده
منابع مشابه
Role of OHVIRA syndrome in renal agenesis: a case report
A 13-year-old female was admitted with abdominal pain and dysmenorrhea. Ultrasonography and magnetic resonance imaging revealed OHVIRA syndrome (uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis). A left hysterotomy was performed. The patient recovered fully following treatment with vaginal septum resection and drainage of a hematometrocolpos.
متن کاملObstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome.
Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare congenital abnormality of the female urogenital tract. We reported OHVIRA syndrome in a 15-year-old girl, who was referred to King Faisal Specialist Hospital and Research Centre, due to hematocolpos and an imperforate hymen. The patient was diagnosed as having an absent right kidney since childhood. She presented wi...
متن کاملWolffian Origin of Vagina Unfolds the Embryopathogenesis of OHVIRA (Obstructed Hemivagina and Ipsilateral Renal Anomaly) Syndrome and Places OHVIRA as a Female Counterpart of Zinner Syndrome in Males
BACKGROUND The classical theory of Müllerian origin of upper vagina fails to explain complex urogenital malformations like OHVIRA syndrome; the Acien's hypothesis, however, unravels the hidden embryopathogenesis. As per Acien, Wolffian (mesonephric) ducts instead of Müllerian ducts and sinovaginal bulbs, give rise to the vagina. The new hypothesis, however, retains the concept of origin of the ...
متن کاملClinical Implications of Obstructed Hemivagina and Ipsilateral Renal Anomaly (OHVIRA) Syndrome in the Prepubertal Age Group
PURPOSE Obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome is a rare syndrome characterized by Müllerian duct and renal anomalies. It is usually regarded as a disease of adolescence; however, due to a number of possible problems, the management of patients before puberty should not be overlooked. We assessed the clinical course of prepubertal patients to propose appropriate m...
متن کاملUncommon presentations of an uncommon entity: OHVIRA syndrome with hematosalpinx and pyocolpos
Müllerian malformations result from defective fusion of the Müllerian ducts during development of the female reproductive system. The least common form of these malformations is Herlyn-Werner-Wunderlich syndrome characterized by obstructed hemivagina and ipsilateral renal anomaly (OHVIRA). The most common presentation of this syndrome is a mass secondary to hematocolpos, pain, and dysmenorrhea....
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ژورنال
عنوان ژورنال: Donald School Journal of Ultrasound in Obstetrics and Gynecology
سال: 2019
ISSN: 0973-614X,0975-1912
DOI: 10.5005/jp-journals-10009-1589